Caroli disease carolis disease carolis syndrome caroli syndrome carolis disease carolis syndrome disease, caroli. Caroli s disease is characterized by the presence of cystic dilatations of the intrahepatic bile ducts. Es una enfermedad hepatica congenita poco frecuente caracterizada por dilataciones. Carolis disease is defined as a abnormal dilatation of the intrahepatica bile ducts. Aunque existen datos diferenciales entre ambas enfermedades renales poliquisticas. Liver transplantation in patients with carolis disease and cholangitis. Puede presentarse a cualquier edad y afecta principalmente a mujeres. Foi descrita primeiramente no ano de1958, em paris, pelo gastroenterologista jacques caroli. Dilatation congenitale des voies biliares in trahepatiques. Enfermedades fibropoliquisticas congenitas hepaticas medicine. The role of surgery in carolis disease request pdf. Its incidence is extremely low 1 in 1,000,000 population and in most of the cases the whole liver is interested and liver transplantation is the treatment of choice. Recurrent cholangitis in a patient with autosomal dominant. Oct 15, 2016 autosomal dominant polycystic kidney disease adpkd is an inherited disorder mainly associated with renal cyst formation and renal function deterioration.
Caroli s disease is defined as a abnormal dilatation of the intrahepatica bile ducts. Intrahepatic cysts are the most common hepatic complication of adpkd. Liver transplantation in patients with caroli s disease and cholangitis. In case of dilatation limited to the left or right lobe, liver resection can be performed. The role of surgery in carolis disease article in journal of the american college of surgeons 2026.
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